Medical Central Resource
Abdominal Aortic Coarctation due to Neurofibromatosis
John Leyendecker
3/26/96
Presentation
17 year old male with known Neurofibromatosis.
Imaging Technique
Angio/Interventional
Angio
Imaging Findings
Severe diffuse narrowing of abdominal aorta with : left renal artery stenosis and aneurysm, replaced right hepatic artery and enlarged internal mammary arteries, which serve as collaterals to the lower extremities.
Diagnosis
Abdominal Aortic Coarctation due to Neurofibromatosis
Discussion
Abdominal aortic coarctation, renal artery stenosis and renal artery aneurysm are all features of Neurofibromatosis with vascular involvement. Other causes of abdominal aortic coarctation include Takayasu's arteritis, fibromuscular disease, radiation-induced arteritis and William Syndrome (idiopathic hypercalceria). Unlike atherosclerotic disease, these entities typically produce smooth, gradually tapering stenoses.
Submitted by: John Leyendecker,Maj,USAF,MC,Wilford Hall Medical Center
Reviewed by: Stephen Johnson,Maj,USAF,MC,Wilford Hall Medical Center
